Reversibility of bronchiectasis in Kartagener’s syndrome: patient’s right to high quality health care services

Abstract

Kartagener’s syndrome is a rare autosomal recessive genetic disease with progressive damage of the respiratory system and situs inversus. Although the management of patients with Kartagener’s syndrome remains uncertain and evidence is limited, it is important to follow up these patients with an adequate and shared care system. This report presents a clinical case of Kartagener’s syndrome in a 25-year-old woman. Computed tomography showed dextrocardia and bronchiectasis. After 7 years, good treatment results were achieved: radiological findings and lung function were improved. The present case demonstrates the complex interrelationship among genetic variation and a proper nonspecific management of Kartagener’s syndrome. Keywords: bronchiectasis, reversibility, Kartagener’s syndrome